대한흉부영상의학회 Korean Society of Thoracic Radiology

Discussion

Diagnosis With Brief Discussion

Courtesy

Samsung Medical Center

Discussion

- Rare benign disorder caused by proliferation of acellular collagen and fibrous tissue within the mediastinum
- Etiology: idiopathic, (?) granulomatous infection in mediastinum
- Clinical features: related to obstruction or compression of vital mediastinal structures
- Two types
Focal type (82%): localized, calcified mass in the paratracheal or subcarinal regions of the mediastinum or in the pulmonary hila
Diffuse type (18%): diffusely infiltrating, often noncalcified mass that affects multiple mediastinal compartments
- Imaging findings:
infiltrative mass of soft-tissue attenuation obliterating normal mediastinal fat planes and encasing or invading adjacent structures
often middle mediastinum involvement (subcarinal and right paratracheal regions); calcification within the mediastinum and hila (86%)
- Treatment and prognosis: unpredictable course
- CT and MR imaging play a vital role in the diagnosis and management of fibrosing mediastinitis

Keywords

Mediastinum, Non-infectious inflammation,